An operation called the Kasai procedure is done to connect the liver to the small intestine, bypassing the malformed ducts. It is most successful if performed before the baby is 10 - 12 weeks old. However, a liver transplant may still ultimately be required.
Expectations (prognosis):
Early surgical intervention will improve the survival of more than one-third of those affected by the condition. The long-term benefit of liver transplant is not yet known, but is expected to improve survival.
Complications:
Liver failure
Infection
Surgical complications
Failure of the Kasai procedure
Irreversible cirrhosis
Calling your health care provider:
Call your health care provider if your child appears jaundiced, or if other symptoms suggestive of this disorder develop.
Review Date: 10/22/2004
Reviewed By: Brendan T. Campbell, MD, MPH, Department of Surgery, Arkansas Children's Hospital, Little Rock, AR. Review provided by VeriMed Healthcare Network.
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